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Morphologic appearance of EH skin. Shown is a semithin section (0

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1 Morphologic appearance of EH skin. Shown is a semithin section (0
Morphologic appearance of EH skin. Shown is a semithin section (0.75 mm) of skin from a patient with severe EH. Basal layer (BL) is normal. Spinous layers (SP), granular layers (GR), and stratum corneum (SC) display cytolysis and hyperthickening. (Courtesy of Dr. Q-C Yu and Dr. E. Fuchs.) Source: Disorders of Intermediate Filaments and Their Associated Proteins, The Online Metabolic and Molecular Bases of Inherited Disease Citation: Valle D, Beaudet AL, Vogelstein B, Kinzler KW, Antonarakis SE, Ballabio A, Gibson K, Mitchell G. The Online Metabolic and Molecular Bases of Inherited Disease; 2014 Available at: Accessed: October 14, 2017 Copyright © 2017 McGraw-Hill Education. All rights reserved

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