-HA -HB -Factor XI deficiency -Factor II deficiency -Factor V deficiency -Factor XIII deficiency -Factor VII deficiency Dental problems in Hemophilia
-Severe Deficiency (Less than 1%) -Moderate Deficiency (less than 1%) -Moderate Deficiency (1%-5%) -Mild Deficiency (≥ 5%) Precoagolant classification
-Frequent bleeding -Two or four per month -Common sites (Joint, muscle, skin) -Hemarthrosis -Chronic muscular problems -Debilitating painful arthritis -Knee, elbow, ankle, Hip, shoulder -Pseudotumor in jaw -Mouth laceration Severe deficiency Hemophilia
Hemophilia Infrequently bleeding Only surgery or Trauma
Purified concentration factor Factor through recombinant technology Whole blood, plasma, cryoprecipitate Half life factor VIII, IX Medical Treatment of Hemophilia
(…Continue) Factor VIII concentrate Routine bleeding (40%) Mild VIII Deficiency DDAVP DDAVP Rise of factor VIII Activity/VWF Tachyphylaxis Water Retention Hyponautremia Seizures
Factor IX deficiency Purified coagulation factor IX concentrate Pure production class protrombine complex PCC = factor IX + … Repeated PCC Infusion DIC Level factor (40%) Hemophilia B Treatment
Vonwillbrand disease Subtyping VWF DDAVP (VWF) Other modalities
Inhibitors(28% HA, 3% - 5% )in Severe HB Low Response Rate to factors Continue Hemorrhage Arthritis Degenerative joint disease Viral Infection blood borne Infection AIDS, Hepatitis B,C Complications factor Infusion
Risks to dental staff Acquiring hepatitis B,C Acquiring HIV
Development of a treatment plan in the hemophilia Use of anti fibrinolytics,Dosage Side effect
Pain control in Hemophilia (…Continue) Analgesia Local Anesthesia PDL Injection Infiltration Block Anesthesia
Prevention of Dental Disease Periodontal therapy Restorative procedures Pulp therapy Oral surgery Surgical complications Antibiotic prophylaxis Orthodontic treatment Dental Healthcare protocol in hemophilia
The end Dr. Jabbarifar 2007
Fungal Infection Viral Infection Bacterial Infection Neoplasm's Idiopathic lesions HIV-gingivitis, HIV – Periodontitis. Oral manifestations HIV Infection
The end Dr. Jabbarifar 2007