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CCHD with Low PBF & No PAH

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Presentation on theme: "CCHD with Low PBF & No PAH"— Presentation transcript:

1 CCHD with Low PBF & No PAH
TOF TOF Equivalents DORV+ VSD+ PS D-TGA + VSD+ PS L-TGA + VSD+ PS Tricuspid Atresia + VSD + PS Single Ventricle + PS Truncus Arteriosus with small pulmonary arteries Pulmonary Atresia with IVS PS with ASD Ebsteins Anomaly Of TV

2 CCHD with Low PBF & PAH Eisenmenger’s Syndrome

3 CCHD with High PBF Inter circulatory mixing Venous level: TAPVC Atrial level : Single Atrium, Tricuspid Atresia, HLHS Ventricular level : Single ventricle Arterial level: Truncus Arteriosus Transposition Physiology D TGA Taussing bing anomaly

4 CCHD with Near Normal PBF
Pulmonary Arterio Venous Fistula Anomalous drainage of vena cava to Left Atrium Un roofing of coronary sinus in to Left Atrium

5 Factors affecting age of Presentation in CCHD

6 Factors affecting age of Presentation in CCHD
0-3 days : Changes in Transition Circulation 4-14 days : Closing ductus physiology 2-18 weeks: Low pulmonary vascular resistance Any age: Myocardial dysfunction, Metabolic and idiopathic

7 Factors affecting age of Presentation in CCHD : 0-3 days
Changes in Transition Circulation Parallel non mixing circulation TGA Critically obstructed series circulation- Obstructed TAPVC HLHS & HRHS Critical AS Interrupted aortic arch HRHS Critical PS Severe Ebsteins

8 Factors affecting age of Presentation in CCHD : 4- 14 days
Closing Ductus Physiology Obstructed Pulmonary circulation TOF (Severe) Tricuspid atresia TGA + VSD + PS Single ventricle + PS Obstructed Systemic circulation Severe CoA

9 Factors affecting age of Presentation in CCHD :2 weeks to 18 weeks
Low Pulmonary vascular resistance Shunt lesions with Left to Right shunts Complete AV Canal defect TOF with mild PS Large VSD TAPVC (Non obstructed) TGA + VSD without PA Single ventricle without PS ALCAPA

10 4- 12 months VSD (small to moderate) PDA (small to moderate) ASD
Mild CoA AS Mild to Mod PS Mild to Mod

11 Cardiac causes of CHF according to age

12 Cardiac causes of CHF according to age
IST Day of life HLHS Obstructed TAPVC Endocardial fibroelastosis Large AV fistula Arrythmia : PAT Congenital Severe TR or PR Premature infants with large PDA

13 Cardiac causes of CHF according to age
First week of life HLHS Complete TGA CoA Severe AS

14 Cardiac causes of CHF according to age
During infancy CoA with PDA or VSD Large VSD or PDA or AV Canal defect TAPVC Tricuspid atresia Persistent Truncus DORV TGA with Large VSD ALCAPA Myocarditis

15 CCHD Clinical clues to Diagnosis

16 CCHD with Bounding Pulse
Truncus Arteriosus Pulmonary Atresia with Large PDA or Large MAPCAS TOF with severe AR Eissenmenger PDA with Pulmonary Regurgitation

17 CCHD with Prominent A wave in JVP
TRICUSPID ATRESIA with Restrictive ASD CCHD with Cannon waves (Complete Heart Block) CCTGA Single Ventricle especially Inverted type

18 CCHD with Prominent V wave in JVP
Ebsteins anomaly Eisenmengers with severe TR Pulmonary atresia with IVS and severe TR

19 CCHD with Prominent LV Impulse
TRICUSPID ATRESIA SINGLE VENTRICLE OF LV TYPE TOF with significant AR PULMONARY ATRESIA with IVS TRUNCUS with Truncal Regurgitation to LV

20 CCHD with Wide Split S2 TAPVC EBSTEINS ANOMALY

21 CCHD with Prominent Pulsation in Second Left ICS
Eisenmengers Syndrome CCTGA with L Posed Aorta

22 CCHD with EDM TOF with AR TOF with Absent Pulmonary Valve
Eisenmenger with PR TRUNCUS ARTERIOSUS with Truncal Regurgitation

23 CCHD with Continous Murmer
Pulmonary Atresia with PDA/MAPCAS TOF : Post BT Shunt Supracardiac TAPVC with Venous Hum at Root of Neck

24 CCHD with Tricuspid Regurgitation
Ebsteins anomaly PULMONARY ATRESIA with IVS and SEVERE TR Eisenmenger with TR TOF with AV CANAL Defect, Severe TR

25 CCHD with Dominant Ventricle

26 CCHD with Right ventricle dominance
TOF DORV+VSD+PS D TGA+VSD+PS L TGA+VSD+PS PS+ASD HLHS

27 CCHD with Left Ventricle dominance
Tricuspid Atresia Double inlet Left Ventricle Pulmonary Atresia with IVS Ebsteins Anomaly with Hypoplastic Rt Ventricle Non Restrictive ASD

28 Biventricular Dominance
DORV+VSD D TGA+VSD Tricuspid Atresia with VSD Truncus Arteriosus


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