1. Amyotrophic lateral sclerosis with frontotemporal dementia (ALS-FTD) syndrome as a phenotype of Creutzfeldt-Jakob disease (CJD)? A case report 
Hiroaki Yaguchi, Akiko Takeuchi, Kazuhiro Horiuchi, Ikuko Takahashi, Shinnichi Shirai, Sachiko Akimoto, Katsuya Satoh, Fumio Moriwaka, Ichiro Yabe, Hidenao Sasaki 
Journal of the Neurological Sciences 
Volume 372, Pages (January 2017)
DOI: /j.jns
Copyright © 2016 Elsevier B.V. Terms and Conditions

2. Fig. 1
A) EMG study of the right biceps demonstrated a fasciculation potential (arrow). B) EMG study of the tongue demonstrated a fasciculation potential (arrow). C) DW-MRI of the brain 4months after onset did not reveal high-intensity lesions. D) DW-MRI of the brain 12months after onset revealed high-intensity lesions in the left motor cortex. E) Images reconstructed using the three-dimensional stereotactic surface projection (3D–SSP) technique. After global normalization to mean blood flow for the entire brain, regional cerebral blood flow (rCBF) in each subgroup was compared with that of the normal control group by the Z test. Color-coding represents the statistical significance (Z-score) of the decrease in rCBF. Red represents more significant rCBF reduction. This study at 4months after onset demonstrated hypoperfusion in the bilateral frontal and temporal lobes. R, right; L, left; LAT, lateral; SUP, superior; INF, inferior; ANT, anterior; POST, posterior; MED, medial; GLB, global cerebral body; THL, thalamus; CBL, cerebellum; PNS, pons.
Journal of the Neurological Sciences  , DOI: ( /j.jns )
Copyright © 2016 Elsevier B.V. Terms and Conditions