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Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease.

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Presentation on theme: "Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease."— Presentation transcript:

1 Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease Arnthor Ævarsson, Jacinta L Chuang, R Max Wynn, Stewart Turley, David T Chuang, Wim GJ Hol Structure Volume 8, Issue 3, Pages 277-291 (March 2000) DOI: 10.1016/S0969-2126(00)00105-2

2 Figure 1 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

3 Figure 2 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

4 Figure 3 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

5 Figure 4 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

6 Figure 5 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

7 Figure 6 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

8 Figure 7 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

9 Figure 8 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

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