1. Prevalence of different aetiologies of pulmonary hypertension (PH) in the paediatric population (results from national registries and paediatric cohorts). ▪: idiopathic/heritable pulmonary arterial hypertension; ▒: PH associated with congenital heart diseas...
Prevalence of different aetiologies of pulmonary hypertension (PH) in the paediatric population (results from national registries and paediatric cohorts). ▪: idiopathic/heritable pulmonary arterial hypertension; ▒: PH associated with congenital heart disease (CHD); ▓: PH associated with connective tissue disease; ░: PH associated with lung disease; □: other. Data shown are taken from registries/paediatric cohorts in Switzerland [13], the UK [1], the Netherlands [12] and France [14]. The most common forms of PH in children are idiopathic/heritable pulmonary arterial hypertension, PH associated with CHD and PH associated with lung disease. #: patients with PH associated with CHD were excluded from this cohort; patients shown here were diagnosed with CHD, but this was not thought to be the cause of the PH.
I. Schulze-Neick, and M. Beghetti Eur Respir Rev 2010;19:
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