1. Mitral valve dysplasia syndrome: A unique form of left-sided heart disease 
Lindsay S. Rogers, MD, Amy L. Peterson, MD, J. William Gaynor, MD, Jonathan J. Rome, MD, Paul M. Weinberg, MD, Jack Rychik, MD 
The Journal of Thoracic and Cardiovascular Surgery 
Volume 142, Issue 6, Pages (December 2011)
DOI: /j.jtcvs
Copyright © 2011 The American Association for Thoracic Surgery Terms and Conditions

2. Figure 1
Fetal ultrasound at 34 weeks in a patient with MVDS and a severely dilated left atrium (LA) and left ventricle (LV) compared with a much smaller right atrium (RA) and right ventricle (RV). Color Doppler over the mitral valve shows severe mitral regurgitation, typical in this patient population.
The Journal of Thoracic and Cardiovascular Surgery  , DOI: ( /j.jtcvs )
Copyright © 2011 The American Association for Thoracic Surgery Terms and Conditions

3. Figure 2
Ratio of left heart to right heart area for each patient echo by gestational age. Each circle represents a single fetal echocardiogram at the corresponding gestational age. Patients living with their native hearts are represented by closed black circles. Patients who died or underwent heart transplant are marked by open circles.
The Journal of Thoracic and Cardiovascular Surgery  , DOI: ( /j.jtcvs )
Copyright © 2011 The American Association for Thoracic Surgery Terms and Conditions

4. Figure 3
A, Normal pulmonary venous Doppler pattern. B, Pulmonary venous Doppler pattern with retrograde flow during atrial systole. C, Pulmonary venous Doppler pattern of a patient with severe mitral regurgitation and restrictive atrial septum. There is flow reversal in both atrial and ventricular systole, giving a “double reversal” pattern.
The Journal of Thoracic and Cardiovascular Surgery  , DOI: ( /j.jtcvs )
Copyright © 2011 The American Association for Thoracic Surgery Terms and Conditions

5. Figure 4
Photograph of specimen with MVDS. The mitral valve (MV) appears dysplastic with thickened leaflets that connect, via a fibrous ridge (red arrow) directly to the anterior lateral (AL) and posterior medial (PM) papillary muscles. Severe aortic valve (AV) hypoplasia is seen. Endocardial fibroelastosis (EFE) is seen lining the entire left ventricle.
The Journal of Thoracic and Cardiovascular Surgery  , DOI: ( /j.jtcvs )
Copyright © 2011 The American Association for Thoracic Surgery Terms and Conditions