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Chronic acquired demyelinating polyneuropathies

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Presentation on theme: "Chronic acquired demyelinating polyneuropathies"— Presentation transcript:

1 Chronic acquired demyelinating polyneuropathies
Chronic acquired demyelinating polyneuropathies. Diagnostic flow diagram: Diagnosis of chronic acquired demyelinating polyneuropathy and specific neuropathy syndrome (CIDP, MADSAM, DADS, MMN) is arrived at predominantly by phenotype coupled with EDX assessment. Other supportive testing is applied when necessary to clarify the diagnosis in atypical cases or aid in the identification of secondary causes of chronic acquired demyelinating neuropathy. Abbreviations: CIDP, chronic inflammatory demyelinating polyradiculoneuropathy; MADSAM, multifocal acquired demyelinating sensory and motor neuropathy; DADS, distal acquired demyelinating sensory neuropathy; MMN, multifocal motor neuropathy; CSF, cerebrospinal fluid; MCP, monoclonal protein; IVIg, intravenous immunoglobulin; PLEX, plasma exchange; GM1, GM1 autoantibodies; MAG, myelin associated glycoprotein; HIV, human immunodeficiency virus; POEMS, polyneuropathy, organomegaly, endocrinopathy, monoclonal protein, skin changes. Source: Chronic Inflammatory Demyelinating Polyradiculoneuropathy and Related Neuropathies, Neuromuscular Disorders, 2e Citation: Amato AA, Russell JA. Neuromuscular Disorders, 2e; 2015 Available at: Accessed: October 30, 2017 Copyright © 2017 McGraw-Hill Education. All rights reserved


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