Chapter 105: Craniofacial Disorders Affecting the Dentition: Genetic Yong-Hee Chun, Paul H. Krebsbach, and James P. Simmer

Figure 1 Figure 1 Dental manifestations of teeth from a patient with dentinogenesis imperfecta. The permanent teeth of this patient exhibit the characteristic blue-gray or opalescent appearance associated with dentinogenesis imperfecta (asterisks). The enamel of the posterior teeth has fractured and the underlying dentin has undergone severe attrition. Crowns have been made to control further destruction (arrows). © 2008 American Society for Bone and Mineral Research From the Primer on the Metabolic Bone Diseases and Disorders of Mineral Metabolism, 7 th Edition.

Figure 2 Figure 2 Radiograph of teeth from a patient with dentin dysplasia. The roots are abnormally short or absent (arrows), and the pulp chamber is obliterated (courtesy of Dr. Sharon Brooks). © 2008 American Society for Bone and Mineral Research From the Primer on the Metabolic Bone Diseases and Disorders of Mineral Metabolism, 7 th Edition.

Figure 3 Figure 3 Dental manifestations of vitamin D–dependent rickets type I. The oral photograph shows the dental presentation of a Hispanic patient having short stature for her age. Both the enamel and the dentin are affected throughout the dentition. The oral radiograph (panorex) shows that the teeth generally had short roots with large pulp chambers. The radiodensity of the enamel crown is similar to that of the underlying dentin. Chronic periodontal disease is often associated with this condition (contributed by Dr. Jan C.-C. Hu). © 2008 American Society for Bone and Mineral Research From the Primer on the Metabolic Bone Diseases and Disorders of Mineral Metabolism, 7 th Edition.